| 摘要: |
| 种痘样水疱病样淋巴瘤(HVLL)于1986年最初被Oono T等描述为“种痘样水疱病与恶性淋巴瘤的共存体冶。2008年世界卫生组织(WHO)淋巴造血组织肿瘤分类将种痘样水疱病样淋巴瘤(HVLL)归入儿童EB病毒(EBV)阳性T细胞淋巴组织增生性疾病,而术语种痘样水疱病样淋巴组织增生性疾病(HVLPD)被引入2016年WHO 淋巴肿瘤分类[中,经典种痘样水疱病(HV)、重症种痘样水疱病、种痘样水疱病样淋巴瘤共同构成种痘样水疱病样淋巴组织增殖性疾病的谱系,从淋巴瘤到淋巴组织增生性疾病的重新分类是为了体现该疾病谱的广泛性,包括偶发缓解的惰性病例。现就HVLPD 的临床特点、病因、病理表现和免疫组织化学、鉴别诊断、治疗及预后等研究进展进行综述。 |
| 关键词: |
| DOI:10.13407/j.cnki.jpp.1672-108X.2021.07.017 |
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| Process of Hydroa Vacciniforme-Like Lymphoproliferative Disorder |
| Li Jiaojiao, Xiao Yizhu |
| (Children’s Hospital of Chongqing Medical University, Ministry of Education Key Laboratory of Child Development and Disorders, Chongqing Key Laboratory of Pediatrics, China International Science and Technology Cooperation Base of Child Development and Critical Disorders, Chongqing 400014, China) |
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